ICD-10 CM Code D81.818
- D81 Combined immunodeficiencies
- D81.8 Other combined immunodeficiencies
- D81.81 Biotin-dependent carboxylase deficiency
D81.818
Other biotin-dependent carboxylase deficiency
Inclusion Term
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
- Multiple carboxylase deficiency
Excludes Type 1
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
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