ICD-10 CM Code D81.81
D81.81
Biotin-dependent carboxylase deficiency
Inclusion Term
- Multiple carboxylase deficiency
Excludes Type 1
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
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