ICD-10 CM Code Q85.8
Q85.8
Other phakomatoses, not elsewhere classified
Inclusion Term
- Peutz-Jeghers Syndrome
- Sturge-Weber(-Dimitri) syndrome
- von Hippel-Lindau syndrome
Excludes Type 1
- Meckel-Gruber syndrome (Q61.9)
- ataxia telangiectasia [Louis-Bar] (G11.3)
- familial dysautonomia [Riley-Day] (G90.1)
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