ICD-10 CM Code Q82.2
Q82.2
Congenital cutaneous mastocytosis
Inclusion Term
- Congenital diffuse cutaneous mastocytosis
- Congenital maculopapular cutaneous mastocytosis
- Congenital urticaria pigmentosa
Excludes Type 1
- cutaneous mastocytosis NOS (D47.01)
- diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
- malignant mastocytosis (C96.2-)
- systemic mastocytosis (D47.02)
- urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
- acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
- Sturge-Weber (-Dimitri) syndrome (Q85.8)
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