ICD-10 CM Code M04.2
M04.2
Cryopyrin-associated periodic syndromes
Inclusion Term
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
Excludes Type 2
- Crohn's disease (K50.-)
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