ICD-10 CM Code E88.41
E88.41
MELAS syndrome
Inclusion Term
- Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes
Excludes Type 1
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
- histiocytosis X (chronic) (C96.6)
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