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ICD-10 CM Code E71.54
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.5
Peroxisomal disorders
E71.54
Other peroxisomal disorders
E71.540
Rhizomelic chondrodysplasia punctata
E71.541
Zellweger-like syndrome
E71.542
Other group 3 peroxisomal disorders
E71.548
Other peroxisomal disorders
Excludes Type 1
Schilder's disease (G37.0)
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