ICD-10 CM Code E71.31
- E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
- E71.3 Disorders of fatty-acid metabolism
E71.31
Disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
- E71.311 Medium chain acyl CoA dehydrogenase deficiency
- E71.312 Short chain acyl CoA dehydrogenase deficiency
- E71.313 Glutaric aciduria type II
- E71.314 Muscle carnitine palmitoyltransferase deficiency
- E71.318 Other disorders of fatty-acid oxidation
Excludes Type 1
- peroxisomal disorders (E71.5)
- Refsum's disease (G60.1)
- Schilder's disease (G37.0)
Excludes Type 2
- carnitine deficiency due to inborn error of metabolism (E71.42)
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