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ICD-10 CM Code E71.11
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.1
Other disorders of branched-chain amino-acid metabolism
E71.11
Branched-chain organic acidurias
E71.110
Isovaleric acidemia
E71.111
3-methylglutaconic aciduria
E71.118
Other branched-chain organic acidurias
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